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14Oct2017

CASE REPORTS- Extremity haemangiopericytoma, a case report from Nigeria

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CASE REPORTS- Extremity haemangiopericytoma, a case report from Nigeria

L O Thanni

Abstract
Haemangiopericytoma is an uncommon soft tissue sarcoma of vascular origin. It occurs more frequently in the extremities than elsewhere in the body although it can arise in any organ. Wide surgical excision is the mainstay of treatment. However, adjuvant radiotherapy and chemotherapy are desirable because the malignant nature of this tumour is frequently unpredictable. Adjuvant therapy is recommended for metastases, recurrence and incomplete resection. Long term follow up is essential in all cases as recurrence can occur several years after treatment. Where little or no experience with managing this tumor exists, it is important to be aware of its clinical behaviour and the treatment options, hence this case reports.

Keywords: haemangiopericytoma, sarcoma, tumour, radiotherapy, chemotherapy

 

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